ASS1 Polyclonal Antibody
For reference only. Please follow the manual included in your kit for instructions.
Catalog Number
RD252452A
Western blot analysis of A431 cell lysate using ASS1 Polyclonal Antibody at dilution of 1:300
Product Name
ASS1 Polyclonal Antibody
Catalog Number
RD252452A
Clonality
Polyclonal
Purification Method
Antigen affinity purification
Isotype
IgG
Host
Rabbit
Background
ASS1 is a rate-limiting enzyme in the urea cycle. Citrullinemia type I is an autosomal recessive disorder that is caused by a deficiency of the urea cycle enzyme argininosuccinate synthetase (ASS1). Deficiency of ASS1 shows various clinical manifestations encompassing severely affected patients with fatal neonatal hyperammonemia as well as asymptomatic individuals with only a biochemical phenotype.
Immunogen Information
Immunogen
Fusion protein of human ASS1
Swissprot
P00966
Synonyms
Argininosuccinate synthase 1Argininosuccinate synthaseArgininosuccinate synthetase 1ASSAss-1ass1ASSAASSYCitrulline aspartate ligaseCitrulline--aspartate ligaseCTLN1
Calculated MW
47 kDa
Observed MW
Refer to figures
Gene Accession
BC021676
Applications
Reactivity
Human, Mouse, Rat
Tested Applications
WB,ELISA
Conjugation
Unconjugated
Dilution
WB 1:500-1:2000, ELISA 1:5000-1:10000
Concentration
0.4 mg/mL
Storage Buffer
PBS with 0.05% NaN3 and 40% Glycerol, pH7.4
Storage Instructions
Store at -20°C. Avoid freeze / thaw cycles.
Research Areas