BCKDHB Polyclonal Antibody
For reference only. Please follow the manual included in your kit for instructions.
Catalog Number
RD87274A
Western blot analysis of extracts of mouse pancreas using BCKDHB Polyclonal Antibody at 1:1000 dilution.
Variation
Quantity
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Overview
Product Name
BCKDHB Polyclonal Antibody
Catalog Number
RD87274A
Clonality
Polyclonal
Purification Method
Affinity purification
Isotype
IgG
Host
Rabbit
Background
This gene encodes the E1 beta subunit of branched-chain keto acid dehydrogenase, which is a multienzyme complex associated with the inner membrane of mitochondria. This enzyme complex functions in the catabolism of branched-chain amino acids. Mutations in this gene have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation and feeding problems. Alternative splicing at this locus results in multiple transcript variants.
Immunogen Information
Immunogen
Recombinant fusion protein of human BCKDHB
Gene ID
594
Swissprot
P21953
Synonyms
BCKDHBBCKDE1BBCKDH E1-betaE1BBCKDHE1-beta
Calculated MW
87kDa/90kDa
Observed MW
90kDa
Applications
Reactivity
Mouse
Tested Applications
WB
Conjugation
Unconjugated
Dilution
WB 1:500-1:2000
Concentration
1mg/mL
Storage Buffer
PBS with 0.02% sodium azide,50% glycerol,pH7.3.
Storage Instructions
Store at -20°C Valid for 12 months. Avoid freeze / thaw cycles.